A systematic review on dental perspectives on pycnodysostosis
DOI:
https://doi.org/10.18203/2319-2003.ijbcp20261125Keywords:
Pycnodysostosis, Short stature, High arched palate, DentalAbstract
Pycnodysostosis (PYND) is an inherited bone disorder known as autosomal recessive. Patients with this disorder can be distinguished by the presence of a height smaller than expected for adults as well as smaller limbs with other dental deformities. As this disorder is rarely diagnosed, this review aimed to highlight the various dental findings from case reports and determine the treatment for the same. To date, no definitive therapies have been developed for this disorder. New treatment modalities are needed for the disease, and proper written protocol guidelines must be adopted while treating patients from dental perspectives. Continuous medical education should be provided to undergraduate students so that they would become familiar with the disease. More large-scale clinical trials are needed to determine better outcomes in general.
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