Hemichorea-hemiballismus as a rare presentation of non-ketotic hyperglycemia: a case report

Vijay Kumar, Kotha Vamshi Krishna Patel, Rishav Raj, Divendu Bhushan, Aniketh V. Hegde


Hemichorea-hemiballismus is a hyperkinetic movement disorder on one side of the body resulting from involvement of the contralateral basal ganglia and striatum mainly. A 50-year-old female presented with a 5-days history of choreiform movements affecting the left upper and lower limb along with hemiface. Her plasma glucose was 576 mgl/dl and her urinary ketones were negative suggesting non-ketotic hyperglycemia. Computed tomography revealed hyper-density in right caudate and putamen consistent with diabetic striatopathy. Non-ketotic hyperglycemia is a rare cause of hemichorea-hemiballismus syndrome. Hemichorea-hemiballismus can be an unusual and rare presentation of diabetic elderly population especially females. Early diagnosis and treatment of hyperglycemia yields an excellent prognosis.


Hemichorea-hemiballismus, Nonketotic hyperglycemia, Diabetic striatopathy

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